Richard's Story - SSCD | UCLA Health News

Out of the blue, Richard Barron, 48, woke up deaf in one ear.

The University of Maine women’s basketball coach was ultra-sensitive to noise--the sound of someone loading the dishwasher was excruciating. Even stranger, Richard began hearing his bones creak and his eyelids move.

Far worse was the noise-related brain fog that descended on him inside the raucous basketball gym. He’d call a timeout during a game—only to hear the ref blow a whistle or the band strike up a tune--and forget why he called the timeout.

After his condition forced him on medical leave, Richard retreated to bed, and his wife and three children took turns tip-toing upstairs to share their day in whispers.

Over a period of five months, Richard visited three prestigious medical centers and saw 15 doctors. No one knew what was wrong. Finally, a CT scan of his skull revealed a tiny opening in his ear bone and an audiologist diagnosed him with superior semicircular canal dehiscence (SSCD).

Researching SSCD online, Richard found a webinar by a UCLA Health neurosurgeon. Dr. Isaac Yang offered to review Richard’s records electronically and confirmed the SSCD diagnosis.

Drawn to the minimally invasive approach that Yang pioneered with UCLA ear surgeon Dr. Quinton Gopen, Richard flew across the country for surgery at Ronald Reagan UCLA Medical Center. In the operating room, Yang made a small incision in Richard’s skull and pushed his brain out of the way, allowing Gopen to plug the miniscule hole in his ear.

When Richard awoke, he was ecstatic to realize that the bizarre noises in his head had vanished and his hearing had returned. That night, his wife and he celebrated over dinner in a Los Angeles restaurant.

Gopen and Yang say Richard’s frustrating journey toward diagnosis isn’t unusual. Superior canal dehiscence wasn’t identified until 1998 – a recent enough discovery only now being added to textbooks and taught in medical school. As a result, most physicians are not familiar with the rare syndrome, which affects an estimated 1% of the population.

Learn more about the Semicircular Canal Dehiscence at http://neurosurgery.ucla.edu/s....emicircular-canal-de